Clinical presentation and histopathological correlation of ciliary body medulloepithelioma: A report of four cases.
J Angulo Velásquez, J Sánchez Ortiz, M Buitrago Buenaño et al.
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Case in brief
Four patients with ciliary body medulloepithelioma presented with varied findings, including reduced visual acuity, ocular pain, and secondary glaucoma. Imaging and clinical assessment were correlated with histopathology, which confirmed teratoid and non-teratoid variants, with neuroepithelial proliferation, rosettes, and mesenchymal components in some cases. Management included enucleation and, in one case, orbital exenteration. Clinicopathological correlation established the diagnosis and informed therapeutic decisions.
What made this case unusual
The report highlights a diagnostic pitfall: a child with unilateral neovascular glaucoma may have an apparently normal fundus despite ciliary body medulloepithelioma.
Diagnostic / clinical pearl
In a child with unilateral neovascular glaucoma and an apparently normal fundus, include ciliary body medulloepithelioma in the differential and undertake meticulous ophthalmic evaluation.